About this ingredient
Acid maltase, also known as acid alpha-glucosidase (GAA), is an enzyme found primarily in lysosomes, the structures inside cells that help break down and recycle materials. Its main function is to break down glycogen, a stored form of glucose, into simpler sugars that the body can use.
Acid maltase is important for normal glycogen metabolism, particularly in muscle cells. When the body does not produce enough functional acid alpha-glucosidase, glycogen can accumulate in cells and cause a rare inherited condition called Pompe disease, also known as glycogen storage disease type II.
Acid maltase is an enzyme, not a typical dietary supplement ingredient. It should not be confused with digestive enzyme supplements or maltase enzymes that help digest maltose in the intestine. Anyone researching acid maltase because of suspected Pompe disease or abnormal enzyme test results should consult a qualified healthcare professional.